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DeCS
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Descriptor English:
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Isovaleryl-CoA Dehydrogenase
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Descriptor Spanish:
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Isovaleril-CoA Deshidrogenasa
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Descriptor Portuguese:
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Isovaleril-CoA Desidrogenase
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Synonyms English:
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Isovaleryl CoA Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase
CoA Dehydrogenase, Isovaleryl
Dehydrogenase, Isovaleryl CoA
Dehydrogenase, Isovaleryl-CoA
Dehydrogenase, Isovaleryl-Coenzyme A
Isovaleryl Coenzyme A Dehydrogenase
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Tree Number:
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D08.811.682.660.462
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Definition English:
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A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA). |
History Note English:
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2006(1973)
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Allowable Qualifiers English:
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Record Number:
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50628
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Unique Identifier:
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D050769
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Occurrence in VHL:
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Similar:
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DeCS CID-10 LILACS
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